Klippel-Trenaunay (KT) syndrome is a congenital vascular disorder consisted of a variety of arterial malformations, elongation of the involved limb, and varicose veins. Klippel-Trenaunay syndrome was first reported in 1900 by Klippel and
Trenaunay.
The
etiology remains unknown and the disease is sporadic in occurance.
The vascular malformation, the primary abnormality, may be any type of hemangioma, arteriovenous fistula, or lymphangioma appearing at birth or in infancy. Other associated anomalies include polydactyly, syndactyly, telangiectasia, and
asymmetrical
facial hypertrophy.
We reported a case of 33-year-old male with Klippel-Trenaunay syndrome. He had an hemangioma, nevus flammeus on his left thigh and buttock. It was also associated with the varicosities, phlebolith, and hypertrophy around left leg and visible
elongation
of left lower limb.
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